Primary ciliary dyskinesia in six patients with bronchiectasis
نویسندگان
چکیده
منابع مشابه
cilia in patients with primary ciliary dyskinesia, bronchiectasis, and in normal subjects
A reproducible technique, utilising a graphics tablet and a personal computer for measuring ciliary orientation from electron micrographs of ciliated epithelium, was assessed. Ciliary deviation was measured in 47 normal subjects (mean ciliary deviation ± 1 SD was 14-6 (3.30)), in eight patients with bronchiectasis and normal ciliary function (15.1 (6 50)), and in seven patients with primary cil...
متن کاملOrientation of respiratory tract cilia in patients with primary ciliary dyskinesia, bronchiectasis, and in normal subjects.
A reproducible technique, utilising a graphics tablet and a personal computer for measuring ciliary orientation from electron micrographs of ciliated epithelium, was assessed. Ciliary deviation was measured in 47 normal subjects (mean ciliary deviation +/- 1 SD was 14.6 (3.3 degrees)), in eight patients with bronchiectasis and normal ciliary function (15.1 (6.5 degrees], and in seven patients w...
متن کاملIs resection of bronchiectasis beneficial in patients with primary ciliary dyskinesia?
A retrospective study of 21 patients with primary ciliary dyskinesia (PCD) was done. Thirteen had prior resection of bronchiectasis and eight had not. Information about present complaints was obtained by a questionnaire. The prevalence of present respiratory symptoms was the same in both groups. The surgical patients had more severe disease and 85% of them considered the operation beneficial. S...
متن کاملPrimary ciliary dyskinesia: considerations regarding six cases of Kartagener syndrome.
Primary ciliary dyskinesia (PCD), previously known as immotile cilia syndrome, is an autosomal recessive hereditary disease that includes various patterns of ciliary ultrastructural defects. The most serious form is Kartagener syndrome (KS), which accounts for 50% of all cases of PCD. The incidence of PCD ranges from 1:20,000 to 1:60,000. Since PCD causes deficiency or even stasis of the transp...
متن کاملPrimary ciliary dyskinesia.
Primary ciliary dyskinesia (PCD) is a rare genetic condition that affects the ciliary function of the respiratory tract, sperm tail, cilia of the embryonic node, and fallopian tube. The condition is characterized by impaired ciliary action, leading to recurrent lower-respiratory-tract infections, bronchiectasis, rhino-sinusitis, otitis media, impaired fertility in women, and infertility in men....
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ژورنال
عنوان ژورنال: Pneumonologia i Alergologia Polska
سال: 2016
ISSN: 2299-8292,0867-7077
DOI: 10.5603/piap.2016.0009